[{"data":1,"prerenderedAt":47},["ShallowReactive",2],{"q-nurse-107-1-maternal-pediatric-063":3},{"subject":4,"subjectSlug":5,"subjectFullName":4,"question":6,"related":22},"產兒科護理學","maternal-pediatric",{"id":7,"webId":8,"year":9,"session":10,"subject":4,"number":11,"stem":12,"options":13,"answer":18,"answerNote":19,"images":20,"explanation":21,"freq":10},"nurse-107-1-產兒科護理學-063","nurse-107-1-maternal-pediatric-063",107,1,63,"有關罹患甲基丙二酸血症（Methylmalonic Acidemia）的患童，下列敘述何者錯誤？",{"A":14,"B":15,"C":16,"D":17},"是一種有機酸代謝異常的體染色體隱性遺傳疾病","適時補充葡萄糖靜脈輸液及碳酸鈉，避免酸中毒症狀","大量甲基丙二酸、丙酸等有機酸堆積會造成楓糖漿尿症","未治療會造成嚴重的代謝性酸血症、酮酸血症、昏迷","C",null,[],"本題考點是甲基丙二酸血症(Methylmalonic Acidemia)的疾病特性,要找錯誤敘述。依其代謝機轉,此症因酵素缺陷使甲基丙二酸、丙酸等『有機酸』堆積,屬有機酸血症;而『楓糖漿尿症』是另一種疾病,肇因於支鏈胺基酸代謝障礙,病因不同,故 C 錯誤,選 C。選項 A 正確:此症為有機酸代謝異常的體染色體隱性遺傳病。選項 B 正確:急性期補充葡萄糖靜脈輸液供能,並給碳酸氫鈉矯正酸中毒。選項 D 正確:未治療會導致嚴重代謝性酸血症、酮酸血症甚至昏迷。錯項 C 把兩種先天代謝異常混為一談。",[23,27,31,35,39,43],{"webId":24,"stem":25,"number":10,"year":26,"session":10},"nurse-106-1-maternal-pediatric-001","王女士，產後第 2 天，孕產史為 G 1 P 1 ，為越南籍配偶，由婆婆陪伴照顧，婆婆堅持產後一定要喝生化湯，此時護理師該如何處置？",106,{"webId":28,"stem":29,"number":30,"year":26,"session":10},"nurse-106-1-maternal-pediatric-002","有關現今產科照護發展趨勢的敘述，下列何者正確？",2,{"webId":32,"stem":33,"number":34,"year":26,"session":10},"nurse-106-1-maternal-pediatric-003","許女士，懷孕 30 週，這兩週血壓上升，尿液檢查也有異常反應，醫師給予胎兒生理活動評估（BPP），有關此評估之敘述下列何者正確？",3,{"webId":36,"stem":37,"number":38,"year":26,"session":10},"nurse-106-1-maternal-pediatric-004","下列何者為懷孕之確實徵候？①聽診到胎心音 ②月經未現 ③觸診到胎兒四肢的活動 ④超音波掃描到妊娠囊 ⑤觸摸到胎兒的外形輪廓",4,{"webId":40,"stem":41,"number":42,"year":26,"session":10},"nurse-106-1-maternal-pediatric-005","有關妊娠期婦女胃腸系統平滑肌鬆弛所產生之生理變化，下列何者正確？",5,{"webId":44,"stem":45,"number":46,"year":26,"session":10},"nurse-106-1-maternal-pediatric-006","有關妊娠期泌尿系統的變化情形之敘述，下列何者正確？",6,1783840741765]