[{"data":1,"prerenderedAt":47},["ShallowReactive",2],{"q-nurse-109-1-maternal-pediatric-056":3},{"subject":4,"subjectSlug":5,"subjectFullName":4,"question":6,"related":22},"產兒科護理學","maternal-pediatric",{"id":7,"webId":8,"year":9,"session":10,"subject":4,"number":11,"stem":12,"options":13,"answer":18,"answerNote":19,"images":20,"explanation":21,"freq":10},"nurse-109-1-產兒科護理學-056","nurse-109-1-maternal-pediatric-056",109,1,56,"小銘，2 歲，罹患典型的異戊酸血症（Isovaleric Acidemia），下列敘述何者正確？",{"A":14,"B":15,"C":16,"D":17},"小銘的疾病是一種有機酸代謝異常的體染色體顯性遺傳疾病","大量的異戊酸堆積在體內，小銘的尿液會有明顯的臭腳汗味","小銘急性發作時主要的醫療處置是矯正脫水及呼吸性鹼中毒","小銘可以攝取特殊配方奶，並逐漸增加肉鹼（carnitine）攝取量代號：4106 頁次：6－5","B",null,[],"本題考點在於典型異戊酸血症（Isovaleric Acidemia, IVA）的遺傳、症狀與處置。依生化病理，IVA 是白胺酸（leucine）代謝路徑上 isovaleryl-CoA dehydrogenase 缺陷所致的有機酸血症，大量異戊酸堆積會散發特徵性的「臭腳汗味（sweaty feet odor）」，故 B 正確。A 錯在遺傳模式，IVA 屬體染色體隱性遺傳而非顯性。C 錯在酸鹼判讀，急性發作因有機酸堆積造成的是代謝性酸中毒，而非呼吸性鹼中毒，處置重點為矯正酸中毒與脫水。D 的治療方向雖含特殊配方與 carnitine（肉鹼）補充，但配方應限制白胺酸攝取、肉鹼用於促進毒性代謝物排除，敘述方式與重點不正確。故答案為 B。",[23,27,31,35,39,43],{"webId":24,"stem":25,"number":10,"year":26,"session":10},"nurse-106-1-maternal-pediatric-001","王女士，產後第 2 天，孕產史為 G 1 P 1 ，為越南籍配偶，由婆婆陪伴照顧，婆婆堅持產後一定要喝生化湯，此時護理師該如何處置？",106,{"webId":28,"stem":29,"number":30,"year":26,"session":10},"nurse-106-1-maternal-pediatric-002","有關現今產科照護發展趨勢的敘述，下列何者正確？",2,{"webId":32,"stem":33,"number":34,"year":26,"session":10},"nurse-106-1-maternal-pediatric-003","許女士，懷孕 30 週，這兩週血壓上升，尿液檢查也有異常反應，醫師給予胎兒生理活動評估（BPP），有關此評估之敘述下列何者正確？",3,{"webId":36,"stem":37,"number":38,"year":26,"session":10},"nurse-106-1-maternal-pediatric-004","下列何者為懷孕之確實徵候？①聽診到胎心音 ②月經未現 ③觸診到胎兒四肢的活動 ④超音波掃描到妊娠囊 ⑤觸摸到胎兒的外形輪廓",4,{"webId":40,"stem":41,"number":42,"year":26,"session":10},"nurse-106-1-maternal-pediatric-005","有關妊娠期婦女胃腸系統平滑肌鬆弛所產生之生理變化，下列何者正確？",5,{"webId":44,"stem":45,"number":46,"year":26,"session":10},"nurse-106-1-maternal-pediatric-006","有關妊娠期泌尿系統的變化情形之敘述，下列何者正確？",6,1783840748340]