[{"data":1,"prerenderedAt":48},["ShallowReactive",2],{"q-nurse-109-2-basic-medicine-035":3},{"subject":4,"subjectSlug":5,"subjectFullName":6,"question":7,"related":24},"基礎醫學","basic-medicine","基礎醫學(包括解剖學、生理學、病理學、藥理學、微生物學與免疫學)",{"id":8,"webId":9,"year":10,"session":11,"subject":4,"number":12,"stem":13,"options":14,"answer":19,"answerNote":20,"images":21,"explanation":22,"freq":23},"nurse-109-2-基礎醫學-035","nurse-109-2-basic-medicine-035",109,2,35,"性聯無伽瑪球蛋白血症（X-linked agammaglobulinemia）發病的主要原因，下列何者正確？",{"A":15,"B":16,"C":17,"D":18},"前趨B細胞（pre-B cell）不能分化成B細胞","胸腺發育不良（thymic hypoplasia）","腺嘌呤去胺酶（adenine deaminase；ADA）基因突變","第二級MHC（主要組織相容性抗原複合體）分子缺乏","A",null,[],"本題考點是性聯無伽瑪球蛋白血症(Bruton病)的分子病因。依免疫學,此症因X染色體上的BTK基因突變,使B細胞成熟停滯,前趨B細胞(pre-B cell)無法分化為成熟B細胞,導致血中各類免疫球蛋白幾乎全缺、反覆細菌感染,故正解A。B胸腺發育不良對應的是DiGeorge症候群,屬T細胞缺陷。C腺苷去胺酶(ADA)基因突變造成的是嚴重複合型免疫缺乏(SCID),T、B細胞皆受損。D第二型MHC分子缺乏造成裸淋巴球症候群,影響CD4輔助T細胞活化。故選A。",1,[25,29,32,36,40,44],{"webId":26,"stem":27,"number":23,"year":28,"session":23},"nurse-106-1-basic-medicine-001","下列有關表皮的敘述，何者正確？",106,{"webId":30,"stem":31,"number":11,"year":28,"session":23},"nurse-106-1-basic-medicine-002","下列何者在組織學特徵上可區分為絲球帶（zona glomerulosa）、束狀帶（zona fasciculata）、網狀帶（zona reticularis）？",{"webId":33,"stem":34,"number":35,"year":28,"session":23},"nurse-106-1-basic-medicine-003","顴弓（zygomatic arch）是由顴骨與下列何者共同組成？",3,{"webId":37,"stem":38,"number":39,"year":28,"session":23},"nurse-106-1-basic-medicine-004","下列何者參與形成踝關節？",4,{"webId":41,"stem":42,"number":43,"year":28,"session":23},"nurse-106-1-basic-medicine-005","下列何者是維持背部直立最重要的肌肉？",5,{"webId":45,"stem":46,"number":47,"year":28,"session":23},"nurse-106-1-basic-medicine-006","行走於前臂的內側，並與上臂深層的靜脈會合成腋靜脈的是那一條血管？",6,1783840753629]